剧绉帮㈡ц借跨朵绉帮㈡（跨）借挎х剧剧缂锛ICD-9:288.101ICD-10:D71.X53灞ㄤ锛ㄨ韩,灞绉瀹わ跨,椋箍挎不婚㈡挎不荤稿宠http://www.zgkw.cnユ锛2009-06-03
涓姒杩
㈡ц借跨锛chronicgranulomatousdisease锛CGD锛互ゃ哄娣宸寸骞挎借挎ф瀹充负圭圭浼х缁界己风澶扮浜轰负锋эX-杩ч浼锛灏颁负甯告蹭ч浼锛涓ゆу涓昏缂洪锋涓诲绯荤浜х杩姘у姘瓒筹涓芥姘у姘㈤堕虫ц锛存骞挎ｃ借挎姣ф涓绉搴锛甯告茬х被缁缁缁娴告鼎缁璇ョ剧锛
褰缁绛寮╄ユ轰舵插尽哄舵瑰уㄦ甯告典扮烘（冲）缁杩拌鸿哄や歌烽哥７（nicotinamideadeninedinucleotidephosphate锛NADPH）姘у跺╁灏靛浠NADPH杞Щ冲瀛姘,浠蹇颁骇瓒姘ч寸瀛“煎哥”变CGDｅ垮ㄧNADPH姘у剁浜缂哄け锛涓芥颁骇锋娲绘х瓒姘ч寸瀛朵唬璋骇╋濡杩姘у姘姘㈡哀圭瀛娆℃隘哥锛浠娉浜х“煎哥”
浜涓村琛ㄧ
1.琛ㄧ锛涓辜骞村圭规ゃ哄娣宸寸澶寸寰寰涓鸿姘у姘㈤朵骇锛濡榛茶¤娌锋澶ц甯姘锛寮璧峰ф宸磋虹榧荤缁轰负㈡х垮楠ㄩ杈甯歌澹灞ц借垮磋绐姝ゅ锛灏寮璧疯缃瀹炽㈡ц规郴ㄨ垮跨夸插欢杩
2.骞跺
村澶
甸蓟
惰绐
锋㈡ц规郴
哥垮插欢杩
涓绘妫
界璁℃板藉楂锛浣界变凹拌鸿哄や歌烽哥７革NADP锛姘у舵椿х己涔涓戒骇杩姘у姘瓒姘у╁朵娲绘ф哀锛朵绮缁斤濡缁茬b245锛戒缂轰绮缁姘锛NBT锛杩璇楠缂哄け璇楠寮甯哥╀甯告璐锛楠ㄩ娑瑙娣辫茬缁缁
瀹规璇剧
灏惧ㄥ寸㈡ц借垮娉ㄦ缁搁村浣浜硅灏撅变挎灏炬㈡х锛灏炬猴硅缁瑁癸澶娓哄瑁硅娓澧澶э告剁杩绋涓舰浜灏惧ㄥ存㈡ц借裤浠瑙涓璐ㄥ颁锛煎句舵ц跨ょ稿哄浣椤惧涓圭肩规郴绛锛绗灏惧ㄥ存㈡ц借夸涓村琛ㄧ
浜娌荤
甯搁瑕澶ч绱存缁不锛纾鸿哄跺涔搴ㄨ姘у姘㈢濡缇涓澶с块娴杩璁や负㈡ц借跨棰宸浣浜浜哄ュ悍ソ锛骞跺娲昏抽澹勾涓ラ渚浜楠ㄩ绉绘
棰插
璇ョ剧涓洪浼х剧锛灏规棰叉规寤鸿浜у妫ャ
澹版渚剧稿宠涓浣涓烘ｈ璇娌荤
