前言目的提高对特发性肺含铁血黄素沉着症(以下简称IPH)X线征象的认识,减少误诊。材料与方法对疾内、胃液内找到含铁血黄素巨噬细胞的33例的X线表现综合分析,讨论其X线分型与临床分期的关系及其病理基础。结果一型(隐匿型)相当于临床较早静止期,仅见肺纹理稍增强;二型(毛片型)相当于急性出血期,多表现为双肺中下野毛玻璃状、片状影、心膈角区不透亮;三型(细网型)属临床出血吸收期,多为细网影,同时伴面纱影;四型(网结型)相当于慢性反复发作期,双肺弥漫分布网结状、粟粒状阴影、心影增大;五型(复合型)相当于临床反复发作后遗期,X线表现为以上各型之和。结论X线胸部平片及结合临床资料完全可以诊断本病。
PurposesTodeepenourunderstandingofidiopathicpulmonaryhemosiderosis(IPH)andreducemisdiagnosisMa-terialsandmethodsAcomprehensiveanalysisoftheX-raymanifestationswasmadein33patients.TherelationshipandpathologicfoundationbetweentheX-raytypingandclinicalstageswerediscussedandtheX-raydiagnosticmainpointswerefoundout.Re-sultsType1(thelatenttype)wasequaltotheclinicalearlierrestingstage.Thestrongerlungmarkingswereonlyseen.Type2(thehairflaket...